Anesthetic management of an infant with Zellweger syndrome undergoing closure of patent ductus arteriosus and pulmonary artery banding: A case report
نویسندگان
چکیده
Zellweger syndrome (ZS) is a rare autosomal recessive inherited disorder within the spectrum of peroxisome biogenesis disorders. It is a progressive and fatal disorder with multiple congenital anomalies. There may be some challenges for anesthesiologists in patients with ZS. We report the anesthetic management of an infant with ZS undergoing closure of patent ductus arteriosus and pulmonary artery banding.
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